Vulvovaginal-gingival syndrome: A rare variant of Erosive Lichen planus

The vulvovaginal-gingival syndrome is an uncommon variant of erosive mucosal lichen planus which is characterized by erosions and desquamation of the vulva, vagina, and gingiva that may lead to mucocutaneous scarring and vaginal stricture formation in long time. Due to its progression the early diagnosis and treatment through a multidisciplinary approach is essential. Treatment is usually difficult and unforunately there are no evidence based studies in the treatment.
Herein we want to present a 63-year-old female with a 10 year history of erosions over oral and genital region which was consistent with erosive lichen planus histologically. Topical clobetasole propionate cream and systemic acitretin 25mg/d were administered for her initial therapy but on the sixth month of this therapy minimal regression was detected and we have changed this therapy with systemic corticosteroids. Clinical symptoms were regressed almost 50% on 2nd month of this therapy.
We want to present this case to remind this unusual and treatment resistant form of lichen planus in differential diagnoses of erosive lesions of mucosal surfaces.